Ectomesenchymoma: case report and review of the literature


Kosem M., Ibiloglu I., Bakan V., Koseoglu B.

TURKISH JOURNAL OF PEDIATRICS, vol.46, no.1, pp.82-87, 2004 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 46 Issue: 1
  • Publication Date: 2004
  • Title of Journal : TURKISH JOURNAL OF PEDIATRICS
  • Page Numbers: pp.82-87

Abstract

Ectomesenchymoma (EMCH) is a rare tumor that may arise in the brain or soft tissue. This tumor type is defined as a form including ectodermal components represented by neuroblasts or ganglion cells and differentiated mesenchymal structures of various types. The mesenchymal component is most often a rhabdomyosarcoma, but liposarcoma, malignant fibrous histiocytoma, leiomyosarcoma, chondrosarcoma, malignant schwannoma, and osseous elements have also been recorded. We report a case of an abdominal malignant ectomesenchymoma, containing three components, schwannoma, embryonal rhabdomyosarcoma, and ganglion cells, in a four-month-old infant. We also review 43 previously reported cases.