Klippel-Feil syndrome and associated ear anomalies

Yidirim N., Arslanoglu A., Mahirogullari M., Sahan M., Ozkan H.

AMERICAN JOURNAL OF OTOLARYNGOLOGY, vol.29, no.5, pp.319-325, 2008 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 29 Issue: 5
  • Publication Date: 2008
  • Doi Number: 10.1016/j.amjoto.2007.09.009
  • Journal Name: AMERICAN JOURNAL OF OTOLARYNGOLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.319-325
  • Van Yüzüncü Yıl University Affiliated: Yes

Abstract

Background and purpose: Klippel-Feil syndrome (KFS) is a congenital segmentation anomaly of the cervical vertebrae that manifests as short neck, low hair line, and limited neck mobility. Various systemic malformations may also accompany the syndrome including wide variety of otopathologies affecting all 3 compartments of the ear (external, middle, and inner ear) as well as internal acoustic canal and vestibular aqueduct. We aimed to investigate these involvements and their clinical correlates in a group of patients with KFS.