Coronary artery fistulas localized between the coronary arteries and heart chambers are rare congenital abnormalities of the heart. Although surgery is the conventional treatment of these fistulas, transcatheter closure is feasible in selected cases. Herein, we present a case in whom the fistula was localized between the coronary artery and right atrium and successfully closed with an Amplatzer Duct Occluder II. An 11-month-old patient was admitted to our clinic with a continuous murmur. His physical examination revealed no other pathology. Transthoracic echocardiography showed a fistula localized between the coronary artery and right atrium. The fistula was closed antegradely with an Amplatzer Duct Occluder II device. Post-procedural echocardiography revealed no continuous flow across the fistulous tract.